Case Series
Volume 8 Issue 11 - 2021
Congenital Bile Duct Cysts in Adults: Management and Outcome of Clinical Cases

B Bouibaouen*, M Salihoun, M Acharki and N Kabbaj

Functional Endoscopy Department, Ibn Sina Hospital, Rabat, Morocco
*Corresponding Author: : B Bouibaouen, Functional Endoscopy Department, Ibn Sina Hospital, Rabat, Morocco.
Received: September 06, 2021; Published: October 29, 2021




Abstract

Introduction: Congenital cystic dilation of the common bile duct (CDCBD) is a congenital malformation, represented by a segmental ectasia with variable types and dimensions. It’s generally limited to the common bile duct, but an association of the hepatic ducts dilatation can be observed.

Results: We report three clinical cases of congenital cystic dilatation of the common bile duct, over a period of May 2015 to April 2018. The average age is 70 years, with extreme ages of 55 and 85 years. The sex ratio is 1/3 with a female predominance. 1 patient presented an abdominal pain, 1 was revealed by a complication and the diagnosis was accidentally discovered. 1 of our patients presented a cytolysis due to a viral hepatitis. Ultrasound was performed in all 3 patients, and in all 3 cases it demonstrated dilation of the CBD without any obstacle. And bili MRI confirmed the diagnosis. Our patients have not been operated.

Discussion: The classic symptomatic triad of CDCBD is abdominal pain, jaundice, and a palpable abdominal mass. However, the CDCBD can be accidentally discovered. Biological cholestasis and hepatic cytolysis can be found. MRI is currently the reference examination in the diagnosis of CDCBD. Todani's Type I dilation remains by far the most frequent case of CDCBD, followed by type Iva. Main complications of the CDCBD are infections, lithiasis, secondary biliary cirrhosis or malignant degeneration. Endoscopic treatment is done by an endoscopic sphincterotomy to ensure effective biliary drainage. Surgery is the treatment of choice for congenital cystic dilation of the main bile duct. The excision will prevent degeneration of the cyst wall and bile ducts. Percutaneous radiological drainage is indicated in palliative situations.

Conclusion: In patients who have not received surgical management, regular clinical, biological and morphological monitoring is necessary in order to detect the occurrence of any complication at an early stage. However, to date, there are no recommendations on the monitoring of these unoperated patients age of the patients and their medical background is important to analyze, to make the assure the best medical care.

Keywords: Congenital Cystic Dilatation; Common Bile Duct; CDCBD

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Citation: B Bouibaouen., et al. “Congenital Bile Duct Cysts in Adults: Management and Outcome of Clinical Cases”. EC Gastroenterology and Digestive System 8.11 (2021): 120-130.

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