Case Report
Volume 9 Issue 1 - 2020
A Rare Case of Pediatric Blastic Plasmacytoid Dendritic Cell Neoplasm: A Case Report
Mohamed Ahmed Maki Ebrahim1*, Mohamed Almuqamam1, Alyosha Smolarski2, Ying Xian Liu2 and Aziza Sedrak1
1Department of Pediatrics, The Brooklyn Hospital Center, Brooklyn, NY, United states of America
1Department of Pathology, The Brooklyn Hospital Center, Brooklyn, NY, United states of America
*Corresponding Author: Mohamed Ahmed Maki Ebrahim, Department of Pediatrics, The Brooklyn Hospital Center, Brooklyn, NY, United states of America.
Received: October 23, 2019; Published: December 06, 2019




Abstract

Blastic Plasmacytoid Dendritic Cell Neoplasm (BPDCN) is usually diagnosed in men ages 65 - 67 years, presenting with cutaneous lesions. Our patient was a 9-year old male who presented with generalized joint pain and fatigue without evidence of skin involvement. Shortly after diagnosis by flow cytometry and bone marrow biopsy, this child completed 1800cGy cranial radiation therapy and currently undergoing chemotherapy with AALL1231 protocol and has shown complete response. This case is a reminder to clinicians to keep a high-index of suspicion of malignancy in children presenting with vague symptoms and adds to the limited number of BPDCN cases in children, thus acting as reference for physicians treating such patients.

Keywords: Blastic Plasmacytoid Dendritic Cell Neoplasm; Leukemia; Acute Myeloid Leukemia; Pediatrics; Pediatric Oncology

References

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Citation: Mohamed Ahmed Maki Ebrahim., et al. “A Rare Case of Pediatric Blastic Plasmacytoid Dendritic Cell Neoplasm: A Case Report”. EC Paediatrics 9.1 (2020): 01-04.

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